Primary huge retroperitoneal mucinous cystadenoma in an Iranian woman: A case report

Document Type : Case Report


1 Shahid Labbafinejad Hospital, Urology and Nephrology Research Center (UNRC), Shahid Beheshti University of Medical Sciences

2 Shahid Labbafinejad Hospital, Shahid Beheshti University of Medical Sciences

3 Tehran University of Medical Sciences



Primary retroperitoneal mucinous cystadenoma is a rare tumor among women. Herein, we present a 47-year-old Iranian woman complaining of abdominal discomfort since six months ago. Primary evaluation showed normal lab data but a huge retroperitoneal cyst in imaging studies. The patient underwent exploratory laparotomy. A 19x14x8 cm well defined cystic lesion with mild adhesion to lower pole of left kidney and descending colon was noticed. The mass was dissected from the adjacent organs and removed completely without spillage of its content. The histopathologic evaluation of the cyst was compatible with retroperitoneal mucinous cystadenoma. Three years follow up did not show any recurrence of the tumor. To our knowledge less than 50 cases with this pathology have been reported and published in the literature and this case is the second one in Iran. Although primary retroperitoneal mucinous cystadenoma is a very rare entity, it should be considered in differential diagnosis of any retroperitoneal cystic lesion. Since the definitive diagnosis of these lesions is made by histopathologic evaluation, complete resection of them is both diagnostic and therapeutic.